BCKDHA
branched chain keto acid dehydrogenase E1, alpha polypeptide
别名:
BCKDE1A, MSU, MSUD1, OVD1A
物种:
Human BCKDHA (593), Mouse Bckdha (12039), Rat Bckdha (25244), Horse BCKDHA (100068678), chicken BCKDHA (374210), cow BCKDHA (282149), sheep BCKDHA (100145857), Zebrafish bckdha (554124), domestic cat BCKDHA (101087186), domestic guinea pig Bckdha (100715185) ...展开
UniProtKB ID:
基因ID:
- Human(593) Summary: The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Sep 2009]
- Mouse(12039) branched chain ketoacid dehydrogenase E1, alpha polypeptide
- Rat(25244) branched chain ketoacid dehydrogenase E1, alpha polypeptide
- Horse(100068678) branched chain keto acid dehydrogenase E1, alpha polypeptide
- chicken(374210) branched chain keto acid dehydrogenase E1, alpha polypeptide
- cow(282149) branched chain keto acid dehydrogenase E1, alpha polypeptide
- sheep(100145857) branched chain keto acid dehydrogenase E1, alpha polypeptide
- Zebrafish(554124) branched chain keto acid dehydrogenase E1, alpha polypeptide
- domestic cat(101087186) branched chain keto acid dehydrogenase E1, alpha polypeptide
- domestic guinea pig(100715185) branched chain keto acid dehydrogenase E1, alpha polypeptide
- naked mole-rat(101705928) branched chain keto acid dehydrogenase E1, alpha polypeptide
- Domestic Rabbit(100352048) branched chain keto acid dehydrogenase E1, alpha polypeptide
- dog(484488) branched chain keto acid dehydrogenase E1, alpha polypeptide
Custom & Knockdown Gene Products
siRNA
Shop predesigned siRNA that are designed using the proprietary Rosetta Inpharmatics algorithm.
shRNA
Shop the largest, most validated shRNA collection and build your own clone sets.
Custom Gene Products
We offer a comprehensive portfolio of DNA oligos, RNA oligos and predesigned primers.
Antibodies
货号
说明
物种反应性
应用
Anti-BCKDHA antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
物种反应性
human
应用
immunohistochemistry
Anti-BCKDHA, (N-terminal) antibody produced in rabbit, affinity isolated antibody,
物种反应性
bovine, dog, guinea pig, horse, human, mouse, rabbit, rat, sheep
应用
immunohistochemistry
western blot
western blot
Anti-BCKDHA antibody produced in mouse, purified immunoglobulin, buffered aqueous solution,
物种反应性
human
应用
western blot
esiRNA
货号
说明
物种