NEB
nebulin
别名:
NEB177D, NEM2
物种:
Human NEB (4703), Mouse Neb (17996), Rat Neb (311029), Zebrafish neb (566928), fruit fly neb (35293), chicken NEB (374027), domestic cat NEB (101086918), dog NEB (476149), Horse NEB (100057773), sheep NEB (101118671) ...展开
UniProtKB ID:
基因ID:
- Human(4703) Summary: This gene encodes nebulin, a giant protein component of the cytoskeletal matrix that coexists with the thick and thin filaments within the sarcomeres of skeletal muscle. In most vertebrates, nebulin accounts for 3 to 4% of the total myofibrillar protein. The encoded protein contains approximately 30-amino acid long modules that can be classified into 7 types and other repeated modules. Protein isoform sizes vary from 600 to 800 kD due to alternative splicing that is tissue-, species-,and developmental stage-specific. Of the 183 exons in the nebulin gene, at least 43 are alternatively spliced, although exons 143 and 144 are not found in the same transcript. Of the several thousand transcript variants predicted for nebulin, the RefSeq Project has decided to create three representative RefSeq records. Mutations in this gene are associated with recessive nemaline myopathy. [provided by RefSeq, Sep 2009]
- Mouse(17996) nebulin
- Rat(311029) nebulin
- Zebrafish(566928) nebulin
- fruit fly(35293) nebbish
- chicken(374027) nebulin
- domestic cat(101086918) nebulin
- dog(476149) nebulin
- Horse(100057773) nebulin
- sheep(101118671) nebulin
- cow(407121) nebulin
- Domestic Rabbit(100328572) nebulin
- naked mole-rat(101726265) nebulin
- domestic guinea pig(100728002) nebulin
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Antibodies
货号
说明
物种反应性
应用
Monoclonal Anti-Nebulin antibody produced in mouse, clone NB2, ascites fluid,
物种反应性
chicken, vertebrates
应用
immunofluorescence
western blot
western blot
Anti-NEB antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
物种反应性
human
应用
immunohistochemistry
Anti-Nebulin exon 143 Antibody, clone NEB-3F4, ,
物种反应性
human
应用
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
Anti-Nebulin exon 144 Antibody, clone NEB-9H1, ,
物种反应性
human
应用
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
esiRNA
货号
说明
物种